Ecthyma gangrenosum due to Pseudomonas aeruginosa sepsis as initial manifestation of X-linked agammaglobulinemia: a case report

Abstract Background X-linked agammaglobulinemia (XLA, OMIM#300,300), caused by mutations in the Bruton tyrosine kinase (BTK) gene, is a rare monogenic inheritable immunodeficiency disorder. Ecthyma gangrenosum is a cutaneous lesion caused by Pseudomonas aeruginosa that typically occurs in patients w...

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Main Authors: Haixia Huang (Author), Ke Bai (Author), Yueqiang Fu (Author), Jin Yan (Author), Jing Li (Author)
Format: Book
Published: BMC, 2020-12-01T00:00:00Z.
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3rd Floor Main Library

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