A bizarre presentation of Peutz - jegher's syndrome in a 2 year old

• Main Authors: Amir Molaei (Author), Hamidreza Alizadeh Otaghvar (Author), Mohammadreza Tarahomi (Author), Daryanaz Shojaei (Author), Leili Mohajerzadeh (Author), Maryam Baghoori (Author), Feizollah Niazi (Author)
• Format: Book
• Published: Pediatric Surgery Research Center of Shahid Beheshti University of Medical Sciences, 2018-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Peutz - jegher's syndrome (PJS) is a rare autosomal dominant disorder with gastro intestinal and mucosal pigmentations. We present a 2 y/o boy with a lesion prolapsing from his rectum that could not be reducted. We found him to have PJS and a familial history of PJS in his parents.