Epstein-Barr virus-related hemophagocytic lymphohistiocytosis complicated with coronary artery dilation and acute renal injury in a boy with a novel X-linked inhibitor of apoptosis protein (XIAP) variant: a case report

• Main Authors: Ru-Yue Chen (Author), Xiao-Zhong Li (Author), Qiang Lin (Author), Yun Zhu (Author), Yun-Yan Shen (Author), Qin-Ying Xu (Author), Xue-Ming Zhu (Author), Zhen-Jiang Bai (Author), Ying Li (Author)
• Format: Book
• Published: BMC, 2020-10-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background X-linked lymphoproliferative disease (XLP) is a rare inherited X-linked primary immunodeficiency diseases (PID). One such disease, X-linked inhibitor of apoptosis protein (XIAP) deficiency, is characterized by Epstein-Barr virus-related hemophagocytic lymphohistiocytosis (EBV-HLH...