Adult Langerhans cell histiocytosis presenting as metachronous colonic polyps
Langerhans cell histiocytosis (LCH) is a rare disease characterized by proliferation of Langerhans-type cells that express CD1a, Langerin (CD207) and S100 protein. Birbeck granules are a hallmark by ultrastructural examination. LCH presents with a wide clinical spectrum, ranging from solitary lesion...
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University of São Paulo,
2013-03-01T00:00:00Z.
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