Papillon-Lefèvre syndrome: Clinical presentation and literature review

• Asıl Yazarlar: O O Soyele (Yazar), A O Taiwo (Yazar)
• Materyal Türü: Kitap
• Baskı/Yayın Bilgisi: Wolters Kluwer Medknow Publications, 2015-01-01T00:00:00Z.
• Konular: article
• Online Erişim: Connect to this object online.

Background: Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive genodermatosis characterized by a diffused palmoplantar hyperkeratosis and severe early-onset periodontitis. Although the exact pathogenesis of this syndrome is still unknown, however, it has been linked to mutations in the c...