Evaluation of Right Ventricular Function in Patients with Propionic Acidemia-A Cross-Sectional Study

• Main Authors: Alexander Kovacevic (Author), Sven F. Garbade (Author), Friederike Hörster (Author), Georg F. Hoffmann (Author), Matthias Gorenflo (Author), Derliz Mereles (Author), Stefan Kölker (Author), Christian Staufner (Author)
• Format: Book
• Published: MDPI AG, 2023-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

(1) Background: In propionic acidemia (PA), myocardial involvement often leads to progressive cardiac dysfunction of the left ventricle (LV). Cardiomyopathy (CM) is an important contributor to mortality. Although known to be of prognostic value in CM, there are no published data on right ventricular...