Juvenile systemic lupus erythematosus presenting as pancarditis
Abstract Background Systemic lupus erythematosus (SLE) is a chronic autoimmune disease with marked variation in its clinical presentation. Juvenile SLE (jSLE) accounts for 15-20% of all cases and is diagnosed when SLE manifests before 18 years of age. Pancarditis is a rare complication of SLE, regar...
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| Main Authors: | , , , , , , |
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| Format: | Book |
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BMC,
2019-11-01T00:00:00Z.
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| Online Access: | Connect to this object online. |
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| Summary: | Abstract Background Systemic lupus erythematosus (SLE) is a chronic autoimmune disease with marked variation in its clinical presentation. Juvenile SLE (jSLE) accounts for 15-20% of all cases and is diagnosed when SLE manifests before 18 years of age. Pancarditis is a rare complication of SLE, regardless of age of disease onset. Case presentation We report a case of jSLE in a 15 year old Caucasian female presenting with an acute episode of pancarditis and multiorgan dysfunction who was successfully treated with systemic corticosteroids and cyclophosphamide. Conclusion Pancarditis can be a presenting feature of jSLE which was previously unreported. A high index of suspicion for severe cardiac involvement is required at all stages of disease. |
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| Item Description: | 10.1186/s12969-019-0372-z 1546-0096 |