Oral health status of children and young adults with maple syrup urine disease in Turkey

• Main Authors: Elif Ballikaya (Author), Yılmaz Yildiz (Author), Nagihan Koç (Author), Ayşegül Tokatli (Author), Meryem Uzamis Tekcicek (Author), Hatice Serap Sivri (Author)
• Format: Book
• Published: BMC, 2021-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Maple syrup urine disease (MSUD) is an inherited disorder clinically characterized by ketoacidosis, seizures, coma, psychomotor delay, and intellectual disability. The treatment requires a life-long protein-restricted diet, rich in carbohydrates and fats, supplemented with a medi...