Cover Image

Strategies to circumvent the CFTR defect in cystic fibrosis

Saved in:

Bibliographic Details
Main Authors:	Frederic eBecq (Author), Marc eChanson (Author)
Format:	Book
Published:	Frontiers Media S.A., 2013-08-01T00:00:00Z.
Subjects:	article
Online Access:	Connect to this object online.
Tags:	Add Tag No Tags, Be the first to tag this record!

Similar Items

Molecular chaperones as targets to circumvent the CFTR defect in cystic fibrosis
by: Rebecca A Chanoux, et al.
Published: (2012)

CFTR and Ca2+ signaling in cystic fibrosis
by: Fabrice eAntigny, et al.
Published: (2011)

Targeting the intracellular environment in cystic fibrosis: restoring autophagy as a novel strategy to circumvent the CFTR defect
by: Valeria Rachela Villella, et al.
Published: (2013)

Nutritional impact of CFTR modulators in children with cystic fibrosis
by: Margaux Gaschignard, et al.
Published: (2023)

Inflammation and CFTR: Might Neutrophils be the Key in Cystic Fibrosis?
by: V. Witko-Sarsat, et al.
Published: (1999)

CFTR modulators: Shedding light on precision medicine for cystic fibrosis
by: Miquéias Lopes-Pacheco
Published: (2016)

Precision Medicine Based on CFTR Genotype for People with Cystic Fibrosis
by: Haq I, et al.
Published: (2022)

Triplet CFTR modulators: future prospects for treatment of cystic fibrosis
by: Chaudary N
Published: (2018)

The effect of CFTR modulators on structural lung disease in cystic fibrosis
by: L. Clara Mok, et al.
Published: (2023)

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Ubiquitylation as a Novel Pharmaceutical Target for Cystic Fibrosis
by: Ryosuke Fukuda, et al.
Published: (2020)

Stimulation of wild-type, F508del- and G551D-CFTR chloride channels by non toxic modified pyrrolo[2,3-b]pyrazine derivatives
by: Luc eDannhoffer, et al.
Published: (2011)

CFTR Modulators: The Changing Face of Cystic Fibrosis in the Era of Precision Medicine
by: Miquéias Lopes-Pacheco
Published: (2020)

Recent Progress in CFTR Interactome Mapping and Its Importance for Cystic Fibrosis
by: Sang Hyun Lim, et al.
Published: (2018)

Modulators of CFTR protein function in the treatment of cystic fibrosis - a literature review
by: Dariusz Chojęta, et al.
Published: (2022)

The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
by: Isabelle R. McKay, et al.
Published: (2022)

Ouabain mimics low temperature rescue of F508del-CFTR in cystic fibrosis epithelial cells
by: Donglei eZhang, et al.
Published: (2012)

Cystic fibrosis, with a focus on new therapies for causal treatment - CFTR protein modulators
by: Klara Iwaniszyn-Zapołoch, et al.
Published: (2022)

Real-life impact of highly effective CFTR modulator therapy in children with cystic fibrosis
by: Margarete Olivier, et al.
Published: (2023)

Optimizing CFTR modulator therapy management for cystic fibrosis through the ReX platform
by: Karin Yaacoby-Bianu, et al.
Published: (2023)

The Role of Extended <i>CFTR</i> Gene Sequencing in Newborn Screening for Cystic Fibrosis
by: Anne Bergougnoux, et al.
Published: (2020)

Outcomes of children with cystic fibrosis screen positive, inconclusive diagnosis/CFTR related metabolic syndrome
by: Mohini A. Gunnett, et al.
Published: (2023)

CFTR Modulator Therapy Enhances Peripheral Blood Monocyte Contributions to Immune Responses in People With Cystic Fibrosis
by: Katherine B. Hisert, et al.
Published: (2020)

Suburban Residences, and How to Circumvent Them
by: Panton, J. E. (Jane Ellen), 1847-1923

Case Report: Japanese Siblings of Cystic Fibrosis With a Novel Large Heterozygous Deletion in the CFTR Gene
by: Mayumi Kawase, et al.
Published: (2022)

Weight increase in people with cystic fibrosis on CFTR modulator therapy is mainly due to increase in fat mass
by: Marialena Mouzaki, et al.
Published: (2023)

Single-Dose Lentiviral Mediated Gene Therapy Recovers CFTR Function in Cystic Fibrosis Knockout Rats
by: Nicole Reyne, et al.
Published: (2021)

Elexacaftor-Tezacaftor-Ivacaftor: A Life-Changing Triple Combination of CFTR Modulator Drugs for Cystic Fibrosis
by: Mafalda Bacalhau, et al.
Published: (2023)

International Approaches to Management of CFTR-Related Metabolic Syndrome/Cystic Fibrosis Screen Positive, Inconclusive Diagnosis
by: Jane Chudleigh, et al.
Published: (2022)

Functional and Pharmacological Characterization of the Rare CFTR Mutation W361R
by: Arnaud Billet, et al.
Published: (2020)

Double homozygous Cystic Fibrosis Transmembrane Regulator gene (CFTR) mutation: A case series and review of the literature
by: Hanaa Banjar, et al.
Published: (2020)

Integrative chemogenomic analysis identifies small molecules that partially rescue ΔF508‐CFTR for cystic fibrosis
by: Rachel A. Hodos, et al.
Published: (2021)

Unity Is Strength: The Mutual Alliance between CFTR and SLC26A6 as Therapeutic Opportunity in Cystic Fibrosis
by: Marilena Pariano, et al.
Published: (2024)

An association study on contrasting cystic fibrosis endophenotypes recognizes <it>KRT8 </it>but not <it>KRT18 </it>as a modifier of cystic fibrosis disease severity and CFTR mediated residual chloride secretion
by: Becker Tim, et al.
Published: (2011)

Evaluation of the Effectiveness of Using the CFTR Modulator Ivacaftor/Lumacaftor in Children with Cystic Fibrosis in the Sverdlovsk Region (Prospective Cohort Study)
by: Yuliya O. Vasenyova, et al.
Published: (2024)

Uncommon clinical presentation of cystic fibrosis in a patient homozygous for a rare CFTR mutation: a case report
by: Joanna Jaworska, et al.
Published: (2020)

State of the Art on Approved Cystic Fibrosis Transmembrane Conductance Regulator (<i>CFTR</i>) Modulators and Triple-Combination Therapy
by: Aniello Meoli, et al.
Published: (2021)

Compound heterozygous CFTR variants (Q1352H and 5T; TG13) in a Chinese patient with cystic fibrosis
by: Run Guo, et al.
Published: (2024)

CFTR Modulator Therapy with Lumacaftor/Ivacaftor Alters Plasma Concentrations of Lipid-Soluble Vitamins A and E in Patients with Cystic Fibrosis
by: Olaf Sommerburg, et al.
Published: (2021)

Nutritional Status and Circulating Levels of Fat-Soluble Vitamins in Cystic Fibrosis Patients: A Cohort Study and Evaluation of the Effect of CFTR Modulators
by: Michela Francalanci, et al.
Published: (2023)

Nitroxyl: A Novel Strategy to Circumvent Diabetes Associated Impairments in Nitric Oxide Signaling
by: Anida Velagic, et al.
Published: (2020)