Thalassemia Alfa Mayor dengan Mutasi Non-Delesi Heterozigot Ganda
Seorang anak perempuan berusia 3 tahun dengan gejala klinis anemia berat, hepatosplenomegali, dan memerlukan tranfusi darah teratur. Gejala klinis telah timbul saat pasien berusia 3 bulan. Hapusan darah tepi menunjukkan gambaran hipokrom, mikrositosis, dan anisopoikilositosis. Kadar HbA2 normal, HbF...
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Main Authors: | Dina Muktiarti (Author), Pustika Amalia Wahidiyat (Author), Ita M. Nainggolan (Author), Iswari Setianingsih (Author) |
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Format: | Book |
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Badan Penerbit Ikatan Dokter Anak Indonesia,
2016-12-01T00:00:00Z.
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