Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia

• Main Authors: G. Piatti (Author), M. M. De Santi (Author), A. Farolfi (Author), G. V. Zuccotti (Author), E. D'Auria (Author), M. F. Patria (Author), S. Torretta (Author), D. Consonni (Author), U. Ambrosetti (Author)
• Format: Book
• Published: BMC, 2020-04-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Recurrent bacterial infections of the respiratory tract are one of the major clinical features of the primary ciliary dyskinesia (PCD), a rare genetic disease due to malfunctioning of motile cilia. Chronic infections and persistent inflammation of the respiratory system result in...