Loeys-Dietz syndrome as a cause of aortic dissection type A.

• Main Authors: Jany Rodríguez Londres (Author), Roger Ravelo Dopico (Author), Gretell Medina Guirola (Author), Lisbeth González González (Author), Ailema Alemán Fernández (Author)
• Format: Book
• Published: ECIMED, 2011-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Loeys-Dietz syndrome is considered a genetic disorder with autosomic dominant transmission and defined by a characteristic triad: generalized arterialtortuosity and aneurysms, hypertelorism and cleft palate or split uvula. The arterial affection, especially aortic dissection and dilatation, is the m...