A rare metastatic mesenteric malignant PEComa with TSC2 mutation treated with palliative surgical resection and nab-sirolimus: a case report

• Prif Awduron: Luke Meredith (Awdur), Timothy Chao (Awdur), Avinoam Nevler (Awdur), Atrayee Basu Mallick (Awdur), Rajan K. Singla (Awdur), Peter A. McCue (Awdur), Wilbur B. Bowne (Awdur), Wei Jiang (Awdur)
• Fformat: Llyfr
• Cyhoeddwyd: BMC, 2023-04-01T00:00:00Z.
• Pynciau: article
• Mynediad Ar-lein: Connect to this object online.

Abstract Background Malignant perivascular epithelioid cell tumors (PEComas) are exceedingly rare malignant mesenchymal neoplasms with characteristic morphological and immunohistochemical (IHC) patterns. However, some malignant PEComas are poorly differentiated with atypical histopathological featur...