Cowden syndrome: Case report, update and proposed diagnostic and surveillance routines

• Principais autores: Masuma Molvi (Autor), Yugal K Sharma (Autor), Kedarnath Dash (Autor)
• Formato: Livro
• Publicado em: Wolters Kluwer Medknow Publications, 2015-01-01T00:00:00Z.
• Assuntos: article
• Acesso em linha: Connect to this object online.

Cowden syndrome (CS) is an infrequent autosomal dominant multisystem genodermatosis, generally involving the skin, oral mucosa, thyroid, breast and gastrointestinal tract. It is characterized by a late onset in the 2 nd or 3 rd decade of life, an extraordinary potential for malignant transformation,...