Long QT syndrome and left ventricular non-compaction in a family with KCNH2 mutation: A case report

• Main Authors: Thomas Caiffa (Author), Antimo Tessitore (Author), Loira Leoni (Author), Elena Reffo (Author), Daniela Chicco (Author), Biancamaria D'Agata Mottolese (Author), Elisa Rubinato (Author), Giorgia Girotto (Author), Stefania Lenarduzzi (Author), Egidio Barbi (Author), Marco Bobbo (Author), Giovanni Di Salvo (Author)
• Format: Book
• Published: Frontiers Media S.A., 2022-08-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

BackgroundLeft ventricular non-compaction (LVNC) is an abnormality of the myocardium, characterized by prominent left ventricular trabeculae and deep inter-trabecular recesses. Long QT syndrome (LQTS) is a cardiac ion channelopathy presenting with a prolonged QT interval on resting electrocardiogram...