Unmasking of systemic lupus erythematosus in a patient with hemophagocytic lymphohistiocytosis- macrophage activation syndrome (HLA-MAS) and diffuse alveolar hemorrhage

• Main Authors: P. Sukhadiya (Author), P. Kumar (Author), D.S. Meena (Author), A. Kumar P.H (Author), N. Vijayan (Author), P. Garg (Author), M.K. Garg (Author)
• Format: Book
• Published: PAGEPress Publications, 2023-03-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Hemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory syndrome caused by macrophages and cytotoxic T cells with aberrant activation. The primary (genetic) form, which is caused by mutations that affect lymphocyte cytotoxicity and immune regulation, is most prevalent in children, whereas th...