Survival and complications in patients with haemoglobin E thalassaemia in Sri Lanka: a prospective, longitudinal cohort study

• Main Authors: Anuja P Premawardhena, ProfMD (Author), Dileepa Senajith Ediriweera, PhD (Author), Amir Sabouhanian, MSc (Author), Angela Allen, PhD (Author), David Rees, ProfMBBS (Author), Shanthimala de Silva, MD (Author), Windsor Perera, MD (Author), Nimal Katugaha, MD (Author), Mahinda Arambepola, MD (Author), Robert C Yamashita, PhD (Author), Sachith Mettananda, ProfDPhil (Author), Nilam Jiffry, MD (Author), Vikita Mehta, MD (Author), Refai Cader, MD (Author), Dayananda Bandara, MD (Author), Timothy St Pierre, ProfPhD (Author), Giulia Muraca, PhD (Author), Christopher Fisher, PhD (Author), Abirami Kirubarajan, MD (Author), Shawn Khan, MD (Author), Stephen Allen, ProfMD (Author), Sanath P Lamabadusuriya, ProfPhD (Author), David J Weatherall, ProfFRS (Author), Nancy F Olivieri, ProfMD (Author)
• Format: Book
• Published: Elsevier, 2022-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Summary: Background: Worldwide, haemoglobin E β-thalassaemia is the most common genotype of severe β-thalassaemia. The paucity of long-term data for this form of thalassaemia makes evidence-based management challenging. We did a long-term observational study to define factors associated with surviva...