Thrombotic thrombocytopenic purpura with decreased level of ADAMTS-13 activity and increased level of ADAMTS-13 inhibitor in an adolescent

• Main Authors: Eun Mi Yang (Author), Dong Kyun Han (Author), Hee Jo Baek (Author), Young Ok Kim (Author), Myung Geun Shin (Author), Hoon Kook (Author), Tai Ju Hwang (Author)
• Format: Book
• Published: Korean Pediatric Society, 2010-03-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Thrombotic thrombocytopenic purpura (TTP) is a thrombotic microangiopathy characterized by endothelial cell damage, resulting in microangiopathic hemolytic anemia, thrombocytopenia, and various degrees of neurological and renal impairment caused by microvascular thrombi. It is rare in children and f...