Epidemiology and clinical features of PFAPA: a retrospective cohort study of 336 patients in western Sweden

• Main Authors: Karin Rydenman (Author), Hanna Fjeld (Author), Josefine Hätting (Author), Stefan Berg (Author), Anders Fasth (Author), Per Wekell (Author)
• Format: Book
• Published: BMC, 2022-09-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome is generally regarded as the most common autoinflammatory disease, but the epidemiology of the disease is largely unknown. The objectives of this study were to estimate the annual incidence an...