Progressive Familial Intrahepatic Cholestasis in Korea: A Clinicopathological Study of Five Patients

• Main Authors: Hyo Jeong Kang (Author), Soon Auck Hong (Author), Seak Hee Oh (Author), Kyung Mo Kim (Author), Han-Wook Yoo (Author), Gu-Hwan Kim (Author), Eunsil Yu (Author)
• Format: Book
• Published: Korean Society of Pathologists & the Korean Society for Cytopathology, 2019-07-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Background Progressive familial intrahepatic cholestasis (PFIC) is a heterogeneous group of autosomal recessive liver diseases that present as neonatal cholestasis. Little is known of this disease in Korea. Methods The records of five patients histologically diagnosed with PFIC, one with PFIC1 and f...