Fulminant Familial Hemophagocytic Lymphohistiocytosis (FHL) in an infant masquerading septic shock - A case report

• Main Authors: Rohit Kapoor (Author), Prabhas Prasun Giri (Author), Joydeep Das (Author)
• 格式: 图书
• 出版: Wolters Kluwer Medknow Publications, 2016-01-01T00:00:00Z.
• 主题: article
• 在线阅读: Connect to this object online.

Hemophagocytic lymphohistiocytosis (HLH) is a rare but life-threatening disease caused by uninhibited hyperinflammatory reaction that can lead to fulminant, life threatening multi organ failure and whose pathophysiology and clinical characteristics are somehow similar to that of severe sepsis and se...