Severe pulmonary arterial hypertension in a patient with hereditary hemorrhagic telangiectasia and multiple pulmonary and hepatic arteriovenous malformations

• Glavni autori: Sunitha Aramalla (Autor), Srinivas Bhyravavajhala (Autor), Bharathi Vanaparty (Autor), Ramakrishna Narayanan (Autor), Sreekanth Yerram (Autor)
• Format: Knjiga
• Izdano: Wolters Kluwer Medknow Publications, 2022-01-01T00:00:00Z.
• Teme: article
• Online pristup: Connect to this object online.

Hereditary hemorrhagic telangiectasia (HHT) is a genetic disorder in which there is faulty development of the arteries. There is a high incidence of pulmonary hypertension (PH) in these patients, the pathophysiology of which is not fully known. An increase in cardiac output, causing high-output card...