Hailey-Hailey disease: clinical, diagnostic and therapeutic update

• Main Authors: Adriana Maria Porro (Author), Camila Arai Seque (Author), Denise Miyamoto (Author), Diego Vanderlei Medeiros da Nóbrega (Author), Milvia Maria Simões e Silva Enokihara (Author), Claudia Giuli Santi (Author)
• Format: Book
• Published: Sociedade Brasileira de Dermatologia, 2024-09-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Hailey-Hailey disease is a rare genodermatosis described in 1939, with an autosomal dominant inheritance pattern, characterized by compromised adhesion between epidermal keratinocytes. It has an estimated prevalence of 1/50,000, with no gender or race predilection. It results from a heteroz...