Rapid and sustained response to JAK inhibition in a child with severe MDA5 + juvenile dermatomyositis

• Main Authors: Timmy Strauss (Author), Claudia Günther (Author), Anja Schnabel (Author), Christine Wolf (Author), Gabriele Hahn (Author), Min Ae Lee-Kirsch (Author), Normi Brück (Author)
• Format: Book
• Published: BMC, 2023-09-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Juvenile dermatomyositis (jDM) is the most common idiopathic inflammatory myopathy of childhood. Amyopathic or hypomyopathic courses have been described. Case presentation We present the case of a 4-year-old patient with MDA5 antibody positive jDM and interstitial lung disease. I...