Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature

• Main Authors: Hinglaj Saha (Author), Ghosh Tapanjyoti (Author), Somak Biswas (Author), Prafulla Kumar Mishra (Author), Kalyani Saha Basu (Author), Uttara Chatterjee (Author)
• Formato: Libro
• Publicado: Wolters Kluwer Medknow Publications, 2019-01-01T00:00:00Z.
• Subjects: article
• Acceso en liña: Connect to this object online.

Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2...