Evolution of lung pathology in lymphangioleiomyomatosis: associations with disease course and treatment response

• Main Authors: Suzanne Miller (Author), Iain D Stewart (Author), Debbie Clements (Author), Irshad Soomro (Author), Roya Babaei‐Jadidi (Author), Simon R Johnson (Author)
• Format: Book
• Published: Wiley, 2020-07-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Lymphangioleiomyomatosis (LAM) is a rare multisystem disease with a variable clinical course. The lungs are infiltrated by nodules of LAM cells, stromal cells and inflammatory cells, causing lung cysts and respiratory failure. We used immunohistochemical markers in lung biopsy and transplan...