Thoracic Computed Tomography Scan and Bronchoscopy Appearance of Mounier-Kuhn Syndrome: A Case Report

• Main Authors: Liliana Fernández-Trujillo MD (Author), Saveria Sangiovanni MD (Author), Eliana Isabel Morales MD (Author), Luz Fernanda Sua MD, PhD (Author), Carlos Alejandro García MD (Author)
• Format: Book
• Published: SAGE Publishing, 2020-08-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Mounier-Kuhn syndrome (MKS) is a rare congenital disease with an autosomal recessive inheritance pattern, characterized by an enlargement of the trachea and bronchi. MKS is secondary to a thinning of the muscular mucosa and atrophy of the longitudinal muscle and elastic fibers of the tracheobronchia...