Polyunsaturated long-chain fatty acids in hyperphenylalaninemias

• Main Authors: Sara Guillén-López (Author), Romina Rodríguez-Schmidt (Author), Marcela Vela-Amieva (Author)
• 格式: 图书
• 出版: Instituto Nacional de Pediatría, 2014-07-01T00:00:00Z.
• 主题: article
• 在线阅读: Connect to this object online.

Patients with hyperphenylalaninemia (HFA) must follow a restricted protein diet, which deprives them of natural dietary sources of polyunsaturated fatty acids (LC-PUFA) that lead to neurological deficits, not related to high phenylalanine blood levels. There is strong evidence of the benefits of doc...