Unusual manifestations of Peutz-Jegher's syndrome in children

PeutzJegher's syndrome (PJS) is a rare, autosomal dominant disease, characterized by gastrointestinal (GI) polyps and perioral hyperpigmentation along with the increased risk of certain malignancies. In children, the most common presentation is recurrent intussusception due to polyps. These pol...

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Autors principals: Sravanthi Vutukuru (Autor), Shailesh Solanki (Autor), Prema Menon (Autor), Ram Samujh (Autor), Sadhna B Lal (Autor)
Format: Llibre
Publicat: Wolters Kluwer Medknow Publications, 2022-01-01T00:00:00Z.
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