Hemophagocytic lymphohistiocytosis resulting from a cytokine storm triggered by septicemia in a child with chronic granuloma disease: a case report and literature review

• Main Authors: Ang Wei (Author), Honghao Ma (Author), Liping Zhang (Author), Zhigang Li (Author), Qing Zhang (Author), Dong Wang (Author), Li Zhang (Author), Hongyun Lian (Author), Rui Zhang (Author), Tianyou Wang (Author)
• Format: Book
• Published: BMC, 2020-03-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Hemophagocytic lymphohistiocytosis (HLH) is a rare potentially fatal illness characterized by impaired natural killer and cytotoxic T cell function. Chronic granulomatous disease (CGD) is an inherited immune deficiency caused by a defect in the nicotinamide adenine dinucleotide p...