Case Report: Anesthetic Management and Electrical Cardiometry as Intensive Hemodynamic Monitoring During Cheiloplasty in an Infant With Enzyme-Replaced Pompe Disease and Preserved Preoperative Cardiac Function

• Main Authors: Meng-Chen Liu (Author), Ming-Tse Wang (Author), Philip Kuo-Ting Chen (Author), Dau-Ming Niu (Author), Yu-Hsuan Fan Chiang (Author), Ming-Hui Hsieh (Author), Hsiao-Chien Tsai (Author)
• Format: Book
• Published: Frontiers Media S.A., 2021-12-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Introduction: Pompe disease is caused by deficiency of the lysosomal enzyme acid α-glucosidase, which results in cardiac and muscular complications that can jeopardize perioperative outcomes. We report a 4-month-old infant with Pompe disease receiving cheiloplasty under general anesthesia with the a...