Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case

• Main Authors: Fernando Peixoto Ferraz de Campos (Author), Elizabeth In Myung Kim (Author), Luciana Andréa Avena Smeili (Author), Patrícia Picciarelli de Lima (Author), Fabiana Roberto Lima (Author), Angélica Braz Simões (Author), Maria Claudia Nogueira Zerbini (Author)
• Format: Book
• Published: University of São Paulo, 2012-06-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...