Enzyme replacement therapy in paediatric patients affected by Anderson-Fabry disease leads to improvement in arterial elasticity, but not normalization

• Main Authors: Pier Paolo Bassareo (Author), Claudio Barbanti (Author), Andrea Raffaele Marras (Author), Giuseppe Mercuro (Author)
• Format: Bog
• Udgivet: Hygeia Press di Corridori Marinella, 2017-07-01T00:00:00Z.
• Fag: article
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Introduction: Increase in blood pressure, probably due to an impairment in arterial elasticity, is frequent in patients affected by Anderson-Fabry disease (FD). The purpose of this study was to evaluate arterial distensibility in a group of children or adolescent with FD before and after enzyme repl...