A Drosophila model for the Zellweger spectrum of peroxisome biogenesis disorders

• Үндсэн зохиолчид: Fred D. Mast (Зохиогч), Jing Li (Зохиогч), Maninder K. Virk (Зохиогч), Sarah C. Hughes (Зохиогч), Andrew J. Simmonds (Зохиогч), Richard A. Rachubinski (Зохиогч)
• Формат: Ном
• Хэвлэсэн: The Company of Biologists, 2011-09-01T00:00:00Z.
• Нөхцлүүд: article
• Онлайн хандалт: Connect to this object online.

SUMMARY Human peroxisome biogenesis disorders are lethal genetic diseases in which abnormal peroxisome assembly compromises overall peroxisome and cellular function. Peroxisomes are ubiquitous membrane-bound organelles involved in several important biochemical processes, notably lipid metabolism and...