Evaluation of Lymphoproliferative Disease and Increased Risk of Lymphoma in Activated Phosphoinositide 3 Kinase Delta Syndrome: A Case Report With Discussion

Activated phosphoionositide-3 kinase delta syndrome (APDS) is a rare disorder caused by activating mutations in phosphoionositide 3-kinase delta (PI3Kδ). This syndrome usually presents in childhood with recurrent sinopulmonary infections and immune deficiency as is seen in the case discussed in this...

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Huvudskapare: Michele N. Pham (Författare, medförfattare), Charlotte Cunningham-Rundles (Författare, medförfattare)
Materialtyp: Bok
Publicerad: Frontiers Media S.A., 2018-12-01T00:00:00Z.
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