Progressive, refractory macrophage activation syndrome as the initial presentation of anti-MDA5 antibody positive juvenile dermatomyositis: a case report and literature review

• Autores principales: J. Alex Stewart (Autor), Theresa Price (Autor), Sam Moser (Autor), Dolores Mullikin (Autor), Angela Bryan (Autor)
• Formato: Libro
• Publicado: BMC, 2022-02-01T00:00:00Z.
• Materias: article
• Acceso en línea: Connect to this object online.

Abstract Background Macrophage activation syndrome (MAS) is a severe and under-recognized complication of rheumatologic diseases. We describe a patient who presented with rapidly progressive, refractory MAS found to have anti-MDA5 antibody Juvenile Dermatomyositis (JDM) as her underlying rheumatolog...