A case of disseminated extranodal Rosai-Dorfman disease diagnosed by skin manifestations

Abstract Rosai-Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969. While classical/nodal RDD is typical, extranodal involvement is seen in up to 43% of all cases, with 23% showing...

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Autores principales: Shintaro Saito (Autor), Akihiko Uchiyama (Autor), Yayoi Shibusawa (Autor), Sei‐ichiro Motegi (Autor)
Formato: Libro
Publicado: Frontiers Media S.A., 2023-06-01T00:00:00Z.
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