A case of disseminated extranodal Rosai-Dorfman disease diagnosed by skin manifestations
Abstract Rosai-Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969. While classical/nodal RDD is typical, extranodal involvement is seen in up to 43% of all cases, with 23% showing...
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| Main Authors: | , , , |
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| Format: | Book |
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Frontiers Media S.A.,
2023-06-01T00:00:00Z.
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| Summary: | Abstract Rosai-Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969. While classical/nodal RDD is typical, extranodal involvement is seen in up to 43% of all cases, with 23% showing only extranodal lesions. Here, we present a case of disseminated extranodal RDD, where the initial symptoms were cutaneous manifestations. |
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| Item Description: | 2574-4593 10.1002/cia2.12286 |