A Case of Von Hippel-Lindau Disease Presented with Multiple Pancreatic Cysts and Medullary Hemangioblastoma

• Main Authors: Young Hyun Kim (Author), Hye Lim Jung (Author), Aram Yang (Author), Ji Hee Kwak (Author), Deok Soo Kim (Author), Jung Yeon Shim (Author), Jae Won Shim (Author)
• Format: Book
• Published: The Korean Society of Pediatric Hematology-Oncology, 2020-04-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Von Hippel-Lindau (VHL) disease is a rare inherited cancer predisposition syndrome characterized by benign and malignant tumors in multiple organs, especially cerebellar hemangioblastomas, retinal angiomas, renal-cell carcinoma, and pheochromocytomas. Clinically, VHL disease also presents an increas...