Successful rituximab treatment for severe rapidly progressive interstitial lung disease with anti-MDA5 antibody-positive juvenile dermatomyositis: a case report and literature review

• Main Authors: Kentaro Nishi (Author), Masao Ogura (Author), Naotaka Tamai (Author), Naofumi Gima (Author), Kentaro Ide (Author), Goro Koinuma (Author), Koichi Kamei (Author), Shuichi Ito (Author)
• Format: Book
• Published: BMC, 2022-08-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Rapidly progressive (RP) interstitial lung disease (ILD) is a life-threatening complication of juvenile dermatomyositis (JDM); however, it is generally refractory to treatment; to the best of our knowledge, no evidence-based treatment has been established for RP-ILD yet. We prese...