Scleromyxedema: clinical diagnosis and autopsy findings

• Main Authors: Ana Carolina Bulhões Sala (Author), Paulo Rowilson Cunha (Author), Clóvis Antônio Lopes Pinto (Author), Célia Antônia Xavier de Moraes Alves (Author), Ingrid Barreto Paiva (Author), Ana Paula Vieira Araujo (Author)
• Format: Book
• Published: Sociedade Brasileira de Dermatologia, 2016-10-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis. Most patients with scleromyxedema have monoclonal gammopathy and systemic...