Familial Hemophagocytic Lymphohistiocytosis secondary to UNC13D mutation: a report of two cases
Abstract Background Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disease characterized by some clinical signs (e.g., non-remitting fever, hepatosplenomegaly) and laboratory findings (e.g., cytopenia, increased ferritin level, hypofibrinogenemia, lipid disorders, coagulopathy, and m...
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BMC,
2022-11-01T00:00:00Z.
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