Case Report: Generalised Panniculitis as a Post-COVID-19 Presentation in Aicardi-Goutières Syndrome Treated With Ruxolitinib

Aicardi-Goutières syndrome (AGS) is a rare hereditary early-onset encephalopathy. The syndrome was first described in 1984, and is characterised by upregulation of the type I interferon (IFN) pathway, which is involved in the host immune response against viral infections, including SARS-CoV-2. Whil...

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Autors principals: Abirami Pararajasingam (Autor), Rachel E. Bradley (Autor), Jennifer Evans (Autor), Ashima Lowe (Autor), Richard Goodwin (Autor), Stephen Jolles (Autor)
Format: Llibre
Publicat: Frontiers Media S.A., 2022-04-01T00:00:00Z.
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3rd Floor Main Library

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