IPEX Syndrome: Improved Knowledge of Immune Pathogenesis Empowers Diagnosis

Immune dysregulation, polyendocrinopathy, enteropathy, X-linked (IPEX) syndrome is a rare monogenic autoimmune disease with variable clinical manifestations, ranging from early-onset severe autoimmunity, including enteropathy, eczema, and type 1 diabetes, to late-onset or atypical symptoms. Despite...

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Main Authors: Federica Barzaghi (Author), Laura Passerini (Author)
Format: Book
Published: Frontiers Media S.A., 2021-02-01T00:00:00Z.
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3rd Floor Main Library

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Call Number: A1234.567
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