Fatal Postpartum Hemorrhage in a Patient with Niemann-Pick Disease Type B

• Κύριοι συγγραφείς: Atakan Tanacan (Συγγραφέας), Abdullah Yalcin (Συγγραφέας), Canan Unal (Συγγραφέας), Seda Banu Akinci (Συγγραφέας), Mehmet Sinan Beksac (Συγγραφέας)
• Μορφή: Βιβλίο
• Έκδοση: Hindawi Limited, 2018-01-01T00:00:00Z.
• Θέματα: article
• Διαθέσιμο Online: Connect to this object online.

Background. Niemann-Pick Disease Type B (NPD B) is a rare lysosomal storage disorder resulting from an inherited deficiency of acid sphingomyelinase activity. Here, we report the case of a splenectomized patient with NPD B who died because of severe postpartum hemorrhage (PPH). Case Presentation. A...