Fatal Postpartum Hemorrhage in a Patient with Niemann-Pick Disease Type B

• Egile Nagusiak: Atakan Tanacan (Egilea), Abdullah Yalcin (Egilea), Canan Unal (Egilea), Seda Banu Akinci (Egilea), Mehmet Sinan Beksac (Egilea)
• Formatua: Liburua
• Argitaratua: Hindawi Limited, 2018-01-01T00:00:00Z.
• Gaiak: article
• Sarrera elektronikoa: Connect to this object online.

Background. Niemann-Pick Disease Type B (NPD B) is a rare lysosomal storage disorder resulting from an inherited deficiency of acid sphingomyelinase activity. Here, we report the case of a splenectomized patient with NPD B who died because of severe postpartum hemorrhage (PPH). Case Presentation. A...