Fatal Postpartum Hemorrhage in a Patient with Niemann-Pick Disease Type B

• Main Authors: Atakan Tanacan (Author), Abdullah Yalcin (Author), Canan Unal (Author), Seda Banu Akinci (Author), Mehmet Sinan Beksac (Author)
• פורמט: ספר
• יצא לאור: Hindawi Limited, 2018-01-01T00:00:00Z.
• נושאים: article
• גישה מקוונת: Connect to this object online.

Background. Niemann-Pick Disease Type B (NPD B) is a rare lysosomal storage disorder resulting from an inherited deficiency of acid sphingomyelinase activity. Here, we report the case of a splenectomized patient with NPD B who died because of severe postpartum hemorrhage (PPH). Case Presentation. A...