Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease

We present a rare presentation of cystic fibrosis with neonatal cholestasis. Histological features of mucoviscidosis were present in liver involving the biliary tract, intestinal mucosa, pancreas, and lung. Besides, there was a rare association with autosomal dominant type of polycystic renal diseas...

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Váldodahkkit: K P Srikanth (Dahkki), Inusha Panigrahi (Dahkki), Babu Ram Thapa (Dahkki), Kim Vaiphei (Dahkki)
Materiálatiipa: Girji
Almmustuhtton: Wolters Kluwer Medknow Publications, 2016-01-01T00:00:00Z.
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3rd Floor Main Library

oažžasuvvan: 3rd Floor Main Library
Hildobáiki: A1234.567
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