Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease

• Main Authors: K P Srikanth (Author), Inusha Panigrahi (Author), Babu Ram Thapa (Author), Kim Vaiphei (Author)
• Format: Knjiga
• Izdano: Wolters Kluwer Medknow Publications, 2016-01-01T00:00:00Z.
• Teme: article
• Online dostop: Connect to this object online.

We present a rare presentation of cystic fibrosis with neonatal cholestasis. Histological features of mucoviscidosis were present in liver involving the biliary tract, intestinal mucosa, pancreas, and lung. Besides, there was a rare association with autosomal dominant type of polycystic renal diseas...