Successful Sirolimus Treatment for Recurrent Pericardial Effusion in a Large Cervicomediastinal Provisionally Unclassified Vascular Anomaly: A Case Report

Provisionally unclassified vascular anomalies (PUVA) are a group of diseases with unique characteristics that make them unclassifiable within vascular tumors or malformations. We describe a PUVA as the cause of recurrent pericardial effusion and its response to sirolimus. A 6-year-old girl was refer...

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Principais autores: Moreno-Alfonso (Autor), San Basilio Berenguer San Basilio Berenguer (Autor), Sarmiento Caldas Sarmiento Caldas (Autor), González Cayón González Cayón (Autor), de la Puente de la Puente (Autor), Triana Triana (Autor), López-Gutiérrez (Autor)
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Publicado em: Georg Thieme Verlag KG, 2023-01-01T00:00:00Z.
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3rd Floor Main Library

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