Successful Sirolimus Treatment for Recurrent Pericardial Effusion in a Large Cervicomediastinal Provisionally Unclassified Vascular Anomaly: A Case Report

• Main Authors: Moreno-Alfonso (Author), San Basilio Berenguer San Basilio Berenguer (Author), Sarmiento Caldas Sarmiento Caldas (Author), González Cayón González Cayón (Author), de la Puente de la Puente (Author), Triana Triana (Author), López-Gutiérrez (Author)
• Format: Book
• Published: Georg Thieme Verlag KG, 2023-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Provisionally unclassified vascular anomalies (PUVA) are a group of diseases with unique characteristics that make them unclassifiable within vascular tumors or malformations. We describe a PUVA as the cause of recurrent pericardial effusion and its response to sirolimus. A 6-year-old girl was refer...